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Duchenne muscular dystrophy and Gower sign

Duchenne Muscular Dystrophy is a common sex-linked recessive trait appearing in 20 to 30 per 100,000 boys. The disease results from absence of a large protein called dystrophin that is associated with the muscle fiber plasma membrane.  
Becker muscular dystrophy arises from an abnormality in the same gene locus that results in the presence of dystrophin that is abnormal in either amount or molecular structure. It has the same clinical symptoms as Duchenne dystrophy, but onset is later, and progression is slower.

Clinically Manifested at about 2 to 3 years of age, boys develop an awkward gait and an inability to run properly. Some have an antecedent history of mild slowness in attaining motor milestones, such as walking and climbing stairs.
By Examination .......> firm calf hypertrophy and mild to moderate proximal leg weakness exhibited by a hyperlordotic, waddling gait and inability to arise from the ground easily. The child typically arises from a lying position on the floor by using his arms to "climb up" his legs and body (Gower sign). Arm weakness is evident by 6 years of age, and most boys are confined to a wheelchair by 12 years of age. By age 16, little mobility of arms remains, and respiratory difficulties increase.
Cause of death :Pneumonia or congestive heart failure resulting from myocardial involvement.

Gower's Sign: